Congenital Anomalies Associated with Trisomy 18 or Trisomy 13: A Registry-Based Study in 16 European Countries, 2000-2011


Por: Springett, A, Wellesley, D, Greenlees, R, Loane, M, Addor, M, Arriola, L, Bergman, J, Cavero-Carbonell, C, Csaky-Szunyogh, M, Draper, E, Garne, E, Gatt, M, Haeusler, M, Khoshnood, B, Klungsoyr, K, Lynch, C, Dias, C, Mcdonnell, R, Nelen, V, O'Mahony, M, Pierini, A, Queisser-Luft, A, Rankin, J, Rissmann, A, Rounding, C, Stoianova, S, Tuckerz, D, Zymak-Zakutnia, N and Morris, J

Publicada: 1 dic 2015 Ahead of Print: 8 sep 2015
Resumen:
The aim of this study was to examine the prevalence of trisomies 18 and 13 in Europe and the prevalence of associated anomalies. Twenty-five population-based registries in 16 European countries provided data from 2000-2011. Cases included live births, fetal deaths (20+ weeks' gestation), and terminations of pregnancy for fetal anomaly (TOPFAs). The prevalence of associated anomalies was reported in live births. The prevalence of trisomy 18 and trisomy 13 were 4.8 (95% CI: 4.7-5.0) and 1.9 (95% CI: 1.8-2.0) per 10,000 total births. Seventy three percent of cases with trisomy 18 or trisomy 13 resulted in a TOPFA. Amongst 468 live born babies with trisomy 18, 80% (76-83%) had a cardiac anomaly, 21% (17-25%) had a nervous system anomaly, 8% (6-11%) had esophageal atresia and 10% (8-13%) had an orofacial cleft. Amongst 240 Live born babies with trisomy 13, 57% (51-64%) had a cardiac anomaly, 39% (33-46%) had a nervous system anomaly, 30% (24-36%) had an eye anomaly, 44% (37-50%) had polydactyly and 45% (39-52%) had an orofacial cleft. For babies with trisomy 18 boys were less likely to have a cardiac anomaly compared with girls (OR = 0.48 (0.30-0.77) and with trisomy 13 were less likely to have a nervous system anomaly [OR = 0.46 (0.27-0.77)]. Babies with trisomy 18 or trisomy 13 do have a high proportion of associated anomalies with the distribution of anomalies being different in boys and girls. (C) 2015 Wiley Periodicals, Inc.

Filiaciones:
Springett, A:
 Wolfson Institute, Queen Mary University of London, London, United Kingdom

Wellesley, D:
 Faculty of Medicine, University of Southampton and Wessex Clinical Genetics Service, Southampton, United Kingdom

Greenlees, R:
 Institute of Nursing Research, University of Ulster, Newtownabbey, United Kingdom

Loane, M:
 Institute of Nursing Research, University of Ulster, Newtownabbey, United Kingdom

Addor, M:
 Division of Medical Genetics, Lausanne, Switzerland

Arriola, L:
 Public Health Division of Gipuzkoa, Instituto BIO-Donostia, Basque Government, CIBER Epidemiologia y Salud Publica - CIBERESP, Spain

Bergman, J:
 Department of Genetics, University Medical Center Groningen, University of Groningen, Groningen, Netherlands

:
 Rare Diseases Research Area, FISABIO-Public Health, Valencia, Spain

Csaky-Szunyogh, M:
 National Public Health and Medical Officer Service (NPHMOS), Budapest, Hungary

Draper, E:
 Department of Health Sciences, University of Leicester, Leicester, United Kingdom

Garne, E:
 Paediatric Department, Hospital Lillebaelt, Kolding, Denmark

Gatt, M:
 Department of Health Information and Research, Guardamangia, Malta

Haeusler, M:
 Medical University of Graz, Graz, Austria

Khoshnood, B:
 INSERM, Paris, France

Klungsoyr, K:
 Department of Global Public Health and Primary Care, University of Bergen, Norway and Medical Birth Registry of Norway, Norwegian Institute of Public Health, Bergen, Norway

Lynch, C:
 Health Service Executive, Kilkenny, Ireland

Dias, C:
 Centro de Estudos e registo de A C, Lisbon, Portugal

Mcdonnell, R:
 Health Service Executive, Dublin, Ireland

Nelen, V:
 Provincial Institute for Hygiene, Antwerp, Belgium

O'Mahony, M:
 Health Service Executive, Cork, Ireland

Pierini, A:
 CNR Institute of Clinical Physiology, Pisa, Italy

Queisser-Luft, A:
 University Medical Center of the Johannes Gutenberg University, Mainz, Germany

Rankin, J:
 Institute of Health and Society, Newcastle University, Newcastle upon Tyne, United Kingdom

Rissmann, A:
 Medical Faculty Otto-von-Guericke University Magdeburg, Magdeburg, Germany

Rounding, C:
 University of Oxford, Oxford, United Kingdom

Stoianova, S:
 St Michael's Hospital, Bristol, United Kingdom

Tuckerz, D:
 Public Health Wales, Swansea, United Kingdom

Zymak-Zakutnia, N:
 Wolfson Institute, Queen Mary University of London, London, United Kingdom

Morris, J:
 Wolfson Institute, Queen Mary University of London, London, United Kingdom
ISSN: 15524825





AMERICAN JOURNAL OF MEDICAL GENETICS PART A
Editorial
Wiley-Liss Inc., 111 RIVER ST, HOBOKEN 07030-5774, NJ USA, Estados Unidos America
Tipo de documento: Article
Volumen: 167 Número: 12
Páginas: 3062-3069
WOS Id: 000367668600023
ID de PubMed: 26347425

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